IJMABHR International Journal of Medical and All Body Health ResearchIJMABHR 2582-8940 Anfo Publication House 100 Congenital Methemoglobinemia in Newborn: Case report SiraPrabhpreet Kaur JainVivek SinghAkhilesh SinghPramod Kumar MBBS, MD Pediatrics, Fortis Hospital, Shalimar Bagh, New Delhi, India MBBS, MRCPCH, FNNF, Fortis Hospital, Shalimar Bagh, New Delhi, India MBBS, DCH, Fellowship Neonatology, Fortis Hospital, Shalimar Bagh, New Delhi, India MBBS, MD, FNNF, Fortis Hospital, Shalimar Bagh, New Delhi, India 2022 3 1 12 14 14122021 01012022 CC BY-NC-SA 4.0

Congenital methemoglobinemia is a rare cause of cyanosis in a newborn. Methemoglobin (MetHb) is a form of haemoglobin (Hb) in which heme iron is oxidized and unable to bind oxygen. The causes of methemoglobinemia are classified as congenital or acquired. We herein report a case of a preterm neonate with cardiopulmonary compromise and cyanosis, eventually diagnosed to have congenital methemoglobinemia. The baby developed cyanosis, which did not improve on oxygen supplementation. Blood gas analysis showed raised Methb levels which was further confirmed by co-oximetry. The baby was started on Oral Vitamin C and improved subsequently and was discharged in a stable condition.

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